Fulminant Childhood Hemophagocytic Syndrome Mimicking Histiocytic Medullary Reticulosis: An Atypical Form of Epstein-Barr Virus Infection
نویسندگان
چکیده
منابع مشابه
Fulminant Epstein-Barr virus-associated hemophagocytic lymphohistiocytosis.
Hemophagocytic lymphohistiocytosis (HLH) is a rare, severe, and often fatal disorder. Its hereditary and sporadic form can present as a significant diagnostic challenge to the otolaryngologist. This report describes two fatal cases of adult patients with HLH initially presented as infectious mononucleosis to an otorhinolaryngologist. The clinical presentation, serological and histological featu...
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Haematologica vol. 85(4):April 2000 3. Magrath IT, Adde M, Shad A, Witts RE, Horak ID. Results in adults with small non-cleaved cell lymphoma treated with a short duration intensive chemotherapy protocol also used in paediatric patients [abstract]. Proceedings ASCO 1994; 1252. 4. Waits TM, Greco FA, Greer JP, et al. Effective therapy for poor-prognosis non-Hodgkin’s lymphoma with 8 weeks of hig...
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There have been a small number of cases of scrub typhus-associated hemophagocytic syndrome (HPS), most of which were treated successfully using adequate antibiotics. Here, we report a case of Epstein-Barr virus (EBV)-associated HPS after scrub typhus infection that was not improved using antirickettsial treatment. A 73-year-old male who had been diagnosed with scrub typhus according to an escha...
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A virus-associated hemophagocytic syndrome is characterized by high fever, liver dysfunction, coagulation abnormalities, pancytopenia, and a benign histiocytic proliferation with prominent hemophagocytosis in bone marrow, lymph node, spleen, and liver. We describe six Japanese children with fatal Epstein-Barr virus (EBV)-associated hemophagocytic syndrome. Five of the six patients had serologic...
متن کاملSplenectomy for histiocytic medullary reticulosis.
ScoTT & Robb-Smith (1939) introduced the term histiocytic medullary reticulosis (HMR) in 1939 to describe a disorder of the reticulo-endothelial system characterized by fever, wasting and generalized lymphadenopathy, associated with splenic and hepatic enlargement and in the final stages jaundice, purpura and anaemia. Necropsy in their patients revealed an intense erythrophagocytosis by histioc...
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ژورنال
عنوان ژورنال: American Journal of Clinical Pathology
سال: 1991
ISSN: 1943-7722,0002-9173
DOI: 10.1093/ajcp/96.2.171